Orthognathic surgery for a patient with trichorhinophalangeal syndrome type I: a case report.
نویسندگان
چکیده
Trichorhinophalangeal syndrome (TRPS) type I is characterized by slowly progressing systemic osseous dysplasia, exhibiting craniofacial and other skeletal deformities. However, there have been few reports describing this syndrome after undergoing orthognathic surgery. In this report, we present a patient with TRPS I who successfully underwent orthognathic surgery. In addition, we examined the skeletal stability of the patient for 2 years after the surgery.
منابع مشابه
Trichorhinophalangeal Syndrome Type I: A Patient with Two Novel and Different Mutations in the TRPS1 Gene
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ورودعنوان ژورنال:
- Oral surgery, oral medicine, oral pathology, oral radiology, and endodontics
دوره 101 2 شماره
صفحات -
تاریخ انتشار 2006